Nchịkọta anwuru anwa zuru ezu

Nchịkọta azụ azụ azụ na-adịghị ala ala (TAPVR) bụ ọrịa obi nke akwara 4 nke na-ewepụ ọbara site na ngụgụ na obi anaghị etinye aka na atrium aka ekpe (ụlọ elu aka ekpe nke obi). Kama nke ahụ, ha na-arapara n'ahụ ọbara ọzọ ma ọ bụ n'akụkụ na-ezighi ezi nke obi. Ọ dị n'oge a na-amụ nwa (ọrịa obi na-efe efe).

Ebumnuche nke ebumnuche nke ikuku azụ azụ amaghị.

Na nrughari nke ọma, a na-eziga ọbara site na ventricle aka nri iji were oxygen na ngụgụ. Ọ na - alọta site na akwara akpa ume (akwara) n'akụkụ aka ekpe nke obi, nke na - eziga ọbara site na aorta na gburugburu ahụ.

Na TAPVR, ọbara oxygen bara ụba na-esi na ngụgụ laghachi na nri atrium ma ọ bụ na akwara nke na-abanye n'ime nri atrium, kama n'akụkụ aka ekpe nke obi. N’ikwu ya n’ụzọ ọzọ, ọbara na-erugharị ma na-esi na ngụgụ apụta, ọ dịghịkwa abanye n’ime ahụ́.

Ka nwa ọhụrụ dị ndụ, nkwarụ atrial septal ntụpọ (ASD) ma ọ bụ patent foramen ovale (ngafe n’etiti aka ekpe na aka nri atria) ga-adịrịrị ka ikwe ka ọbara oxygenated na-asọga n’akụkụ aka ekpe nke obi na akụkụ ahụ ndị ọzọ.

Ọnọdụ dị njọ nke a dabere na-egbochi ma ọ bụ na-egbochi mgbochi akpa ume ka ha na-agbapụ. Obere TAPVR na-ebute ihe mgbaàmà na nwata ma nwee ike ịnwụ ngwa ngwa ma ọ bụrụ na ahụghị ya ma dozie ya na ịwa ahụ.

Nwatakịrị ahụ nwere ike ịda ọrịa nke ukwuu ma nwee ike inwe mgbaàmà ndị a:

• Bulish nke anụ ahụ (cyanosis)
• Ugboro ume iku ume
• Ike ọgwụgwụ
• Ogbenye nri
• Ọganihu na-adịghị mma
• Na-eku ume ngwa ngwa

Mara: Mgbe ụfọdụ, enweghi ihe mgbaàmà ị nwere ike ịpụta na nwata ma ọ bụ na nwata.

Ule nwere ike ịgụnye:

• Mkpụrụ ndụ cardiac nwere ike ikwenye nchoputa site na igosi na akwara ọbara jikọtara onwe ha
• ECG na-egosi ịbawanye nke ventricles (hypertrophy ventricular)
• Echocardiogram nwere ike igosi na arịa pulmonary na-agbakwunye
• MRI ma ọ bụ CT scan nke obi nwere ike igosi njikọ dị n'etiti arịa pulmonary
• X-ray nke obi na-egosi ihe dị mma na obere obi nwere mmiri dị na ngụgụ

Gerywa ahụ iji rụzie nsogbu a chọrọ ozugbo enwere ike. Na ịwa ahụ, eriri akpa ume jikọtara na atrium aka ekpe wee mechie nkwarụ n'etiti aka nri na atrium aka ekpe.

Ọ bụrụ na agwọghị ọnọdụ a, obi ga-ebuwanye ibu, na-eduga na ọdịda obi. Idozi ntụpọ ahụ na mbụ na-enye nsonaazụ dị mma ma ọ bụrụ na enweghị mgbochi nke akwara pulmonary na njikọ ọhụrụ n'ime obi. Antsmụaka amachibidoro veins emeela ka ndụ ha ka njọ.

Nsogbu nwere ike ịgụnye:

• Nsogbu iku ume
• Obi mgbawa
• Oge ufodu, ngwa ngwa obi (arrhythmias)
• Ọrịa akpa ume
• Ọbara mgbali elu

Ọnọdụ a nwere ike pụta ìhè n'oge ọmụmụ. Otú ọ dị, ihe mgbaàmà nwere ike ọ gaghị adị ruo oge ọzọ.

Kpọọ onye na-ahụ maka ahụike gị ma ọ bụrụ na ị hụ mgbaàmà nke TAPVR. A chọrọ nlebara anya ozugbo.

Onweghi uzo a mara iji gbochie TAPVR.

TAPVR; Total veins; Ọrịa obi congenital - TAPVR; Ọrịa obi Cyanotic - TAPVR

• Obi - ngalaba site n'etiti
• Kpamkpam kpam kpam anabataghi akpa ume venous - X-ray
• Kpamkpam kpam kpam adịghị ala ala venous laghachi - x-ray
• Kpamkpam kpam kpam anabataghi akpa ume venous - X-ray

Fraser CD, Kane LC. Ọrịa afọ ime. Na: Townsend CM Jr, Beauchamp RD, Evers BM, Mattox KL, eds. Akwụkwọ Sabiston nke gerywa Ahụ: Ntọala Nduzi nke Omume Ahụhụ Oge a. Agba nke 20. Philadelphia, PA: Elsevier; 2017: isi 58.

Webb GD, Smallhorn JF, Therrien J, Redington AN. Congenital ọrịa obi na okenye na ụmụaka na-enwe ndidi. Na: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. Ọrịa Obi Braunwald: Akwụkwọ ọgụgụ nke Ọgwụ Ọrịa Cardiovascular. Nke 11. Philadelphia, PA: Elsevier; 2019: isi 75.