Odee: Christy White
OfbọChị Okike: 6 Mee 2021
DatebọChị Mmelite: 25 Juunu 2024
Anonim
Phenylketonuria - causes, symptoms, diagnosis, treatment, pathology
Vidio: Phenylketonuria - causes, symptoms, diagnosis, treatment, pathology

Ndinaya

Phenylalanine nwere ike inye aka na njikwa dị arọ n'ihi na ọ na-esonye na usoro na-edozi oriri nri ma na-enye ahụ ahụ mmetụta nke afọ ojuju. Phenylalanine bụ amino acid nke enwere ike ịchọta ya na nri dị na protein, dịka anụ, azụ na mmiri ara ehi na ngwaahịa mmiri ara ehi, yana n'ụdị mgbakwunye ndị erere n'ụlọ ahịa ọgwụ na ụlọ ahịa nri ahụike.

Iji dọkịta ma ọ bụ onye na-edozi ahụ ga-edozi ọgwụ ndị ọzọ nke phenylalanine ma gosipụta ya maka ndị nwere nsogbu dịka ọbara mgbali elu, ọrịa obi na ụmụ nwanyị dị ime.

Omume nke phenylalanine na njikwa agụụ

Phenylalanine na-achịkwa agụụ n'ihi na ọ na-esonye na nguzobe nke dopamine na norepinephrine, ihe ndị dị mkpa maka nhazi nri nri na nke metụtara njikwa agụmakwụkwọ, ọnọdụ na ncheta. Na mgbakwunye, phenylalanine na-akpali mmepụta nke cholecystokinin hormone, nke na-arụ ọrụ n'ime eriri afọ ma na-enye ahụ ahụ afọ ojuju.


Ọ na-abụkarị ọgwụ a tụrụ aro nke phenylalanine bụ 1000 ka 2000 mg kwa ụbọchị, mana ọ na-adị iche dịka njirimara onye ahụ, dị ka afọ, mmega ahụ yana ọnụnọ nke nsogbu dịka nrụgide na nchekasị. Agbanyeghị, mgbakwunye phenylalanine naanị ezughi iji felata, ebe ọ bụ na ibu ibu na-eme naanị mgbe enwekwara ezigbo nri.

Nri dị elu na phenylalaninePhenylalanine mgbakwunye

Nlekọta nke a ga-enwerịrị na mgbakwunye phenylalanine

Ikwesiri ịkpachara anya na phenylalanine supplementation n'ihi na ngafe nke amino acid nwere ike inwe mmetụta dị ka nrịkasi obi, ọgbụgbọ na isi ọwụwa. Phenylalanine na-contraindicated na ikpe nke:


  • Ọrịa obi;
  • Ọbara mgbali elu;
  • Womenmụ nwanyị dị ime ma ọ bụ ndị na-enye ara ara;
  • Ndị na-a drugsụ ọgwụ iji gwọọ ịda mbà n'obi ma ọ bụ nsogbu uche ndị ọzọ;
  • Ndị nwere phenylketonuria.

Ya mere, mgbakwunye nke phenylalanine kwesịrị iduzi dọkịta ma ọ bụ onye na-edozi ahụ iji hụ na ọ bara uru.

Nri dị elu na phenylalanine

Phenylalanine dị na nri dị na protein, dịka anụ, azụ, mmiri ara ehi na ngwaahịa mmiri ara ehi, mkpụrụ, soya, agwa na ọka. Nri nke phenylalanine na nri anaghị eweta ihe egwu ahụike ma naanị ndị nwere phenylketonuria kwesịrị izere nri ndị a. Hụ ndepụta zuru ezu nke nri Phenylalanine bara ọgaranya.

Y’oburu na ichoro ifelata, lee kwa:

  • Iwetulata ibu ngwa ngwa
  • Otu esi eme nri di nma ka ị ghara ibu ibu

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