Odee: Marcus Baldwin
OfbọChị Okike: 20 Juunu 2021
DatebọChị Mmelite: 1 Julai 2025
Anonim
Ihe kpatara XII (Hageman akpata) ụkọ - ỌGwụ
Ihe kpatara XII (Hageman akpata) ụkọ - ỌGwụ

Ebumnuche nke ihe kpatara XII bụ nsogbu a ketara eketa nke na - emetụta protein (ihe nke abụọ) nke metụtara mkpụkọ ọbara.

Mgbe ị na-agba obara, usoro ihe na-eme n’ime ahụ nke na - enyere mkpụkọ ọbara aka. A na-akpọ usoro a coagulation cascade. Ọ gụnyere protein pụrụ iche a na-akpọ coagulation ma ọ bụ ihe mkpụkọ. May nwere ike ịnwe ohere dị elu nke ọbara ọgbụgba ma ọ bụrụ na otu ma ọ bụ karịa n'ime ihe ndị a na-efu ma ọ bụ na ha anaghị arụ ọrụ dịka ha kwesiri.

Ihe kpatara XII bụ otu ihe dị otú ahụ. Enweghị nke a anaghị eme ka ị gbaa ọbara n'ụzọ na-adịghị mma. Ma, ọbara na-ewe ogologo oge karịa ka ọ dị na ya iji kee eriri ule.

Ebumnuche ebumnuche kpatara XII bụ ọrịa na-anaghị ahụkebe eketa

A naghị enwekarị mgbaàmà.

A na-ahụkarị ụkọ ihe kpatara XII mgbe a na-anwale ule ọbara maka oge nyocha.

Ule nwere ike ịgụnye:

  • Ihe nyocha XII iji tụọ ọrụ nke ihe XII
  • Oge thromboplastin na-ele anya (PTT) iji lelee oge ọ ga-ewe ọbara iji kpuchie
  • Inggwakọta ọmụmụ ihe, nyocha PTT pụrụ iche iji gosipụta ihe kpatara ụkọ XII

Ọgwụgwọ anaghị achọkarị.


Ihe ndị a nwere ike ịnyekwu ozi na ụkọ XII:

  • National Hemophilia Foundation - www.hemophilia.org/Bleeding-Disorders/Types-of-Bleeding-Disorders/Other-Factor-Deficiencies/Factor-XII
  • Organizationtù Mba Maka Ọrịa Na-adịghị - rarediseases.org/rare-diseases/factor-xii-deficiency
  • NIH Genesos na Information Center nke Ọrịa - rarediseases.info.nih.gov/diseases/6558/factor-xii-deficiency

Ihe ga-esi na ya pụta ga-adị mma na-enweghị ọgwụgwọ.

Enweghi nsogbu.

Onye nlekọta ahụike na-achọpụtakarị ọnọdụ a mgbe ọ na-agba ule ụlọ nyocha ndị ọzọ.

Nke a bụ nsogbu a ketara eketa. Onweghi uzo amara iji gbochie ya.

F12 erughi; Hageman akpata erughị; Emankpụrụ Hageman; HAF erughi

  • Ọbara ọbara

Gailani D, Wheeler AP, Neff AT. Ọ bụ ụkọ coagulation kpatara erughị eru. Na: Hoffman R, Benz EJ, Silberstein LE, et al, ndị ọzọ. Hematology: ickpụrụ na Omume. Nke 7. Philadelphia, PA: Elsevier; 2018: isi 137.


JElọ Nzukọ JE. Hemostasis na coagulation ọbara. Na: JElọ Nzukọ JE, ed. Akwụkwọ Guyton na Halllọ Akwụkwọ Ahụike Ahụike. Nke 13. Philadelphia, PA: Elsevier; 2016: isi 37.

Ragni MV. Ọrịa ọgbụgba ọbara: ụkọ ihe kpatara nsogbu. Na: Goldman L, Schafer AI, eds. Ọgwụ Goldman-Cecil. Nke iri abụọ na ise. Philadelphia, PA: Elsevier Saunders; 2016: isi 174.

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