Odee: Roger Morrison
OfbọChị Okike: 23 Septemba 2021
DatebọChị Mmelite: 17 Onwa Epurel 2025
Anonim
Introduction to Porphyria | Porphyria Cutanea Tarda vs. Acute Intermittent Porphyria
Vidio: Introduction to Porphyria | Porphyria Cutanea Tarda vs. Acute Intermittent Porphyria

Ndinaya

Mbubreyo akpụkpọ porphyria bụ ụdị kachasị nke porphyria nke na-eme ka obere ọnya pụta na anụ ahụ gosipụtara anyanwụ, dịka azụ aka, ihu ma ọ bụ isi, n'ihi enweghị enzyme nke imeju na-eduga na nchịkọta iron na akpụkpọ ahụ. Cutaneous porphyria enweghị ọgwụgwọ, mana enwere ike ijikwa ya site na iji ọgwụ ndị ọgwụ na-ede.

N'ozuzu, igbu oge porphyria na-apụta n'oge okenye, karịsịa na ndị ọrịa na-a frequentlyụ mmanya na-a frequentlyụkarị ma ọ bụ ndị nwere nsogbu imeju, dịka ịba ọcha n'anya C, dịka ọmụmaatụ.

Mbubreyo akpụkpọ porphyria anaghị abụkarị mkpụrụ ndụ ihe nketa, agbanyeghị, n'ọnọdụ ụfọdụ ọ nwere ike isi na nne na nna gafere ụmụaka, a na-atụ aro ndụmọdụ banyere mkpụrụ ndụ ihe nketa tupu ịtụrụ ime, ma ọ bụrụ na enwere ọtụtụ ikpe na ezinụlọ.

Mgbaàmà nke ọnyá porphyria

Ihe nrịba ama mbu nke porphyria na-egbu onwe ya bu ntoputa nke obere blisters n’ahụ ekpughere n’anyanwụ, nke na-ewe oge iji gwọọ, agbanyeghị, ihe mgbaàmà ndị ọzọ gụnyere:


  • Ikwu okwu too nke ntutu na ihu;
  • Akpụkpọ ahụ siri ike n’ebe ụfọdụ, dịka ogwe aka ma ọ bụ ihu;
  • Mmiri mamịrị gbara ọchịchịrị.

Mgbe ọnya ndị ahụ kwụsịrị, ọnyá ma ọ bụ ntụpọ ọkụ nwere ike ịpụta nke na-ewe ogologo oge iji gwọọ.

Nchoputa nke cutaneous porphyria gha aghaghi ime ya site na onye okacha mara na aru aru site na obara, mmamiri na nsonaazụ nnwale iji gosi na enwere porphyrin n’ime sel, n’ihi na obu ihe ndi nke imeju meputara n’oge oria a.

Ọgwụgwọ maka cutaneous porphyria

Ọgwụgwọ maka cutaneous porphyria ga-abụrịrị onye ọkachamara na-ahụ maka ọgwụ na-arụ ọrụ yana mmekorita ya na onye na-agwọ ọrịa, ebe ọ bụ na ọ dị mkpa ijikwa ọkwa nke porphyrin nke imeju mepụtara. Ya mere, dabere na mgbaàmà nke onye ọrịa, a pụrụ ime ọgwụgwọ site na ọgwụgwọ maka porphyria na-egbu egbu, dị ka chloroquine ma ọ bụ hydroxychloroquine, nkwụsị ọbara mgbe niile iji belata ogo ígwè na sel ma ọ bụ njikọta nke abụọ.

Na mgbakwunye, n'oge ọgwụgwọ a na-atụ aro ka onye ọrịa ahụ zere ị alcoholụbiga mmanya na ikpu anwụ, ọbụlagodi na mkpuchi anwụ, yana ụzọ kachasị mma iji chebe akpụkpọ ahụ site na anyanwụ bụ iji uwe ogologo ọkpa, uwe ogologo aka, okpu na uwe aka, dịka ọmụmaatụ .


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