Odee: Gregory Harris
OfbọChị Okike: 8 Onwa Epurel 2021
DatebọChị Mmelite: 16 Mee 2024
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What is Fuchs’ dystrophy? | Ohio State Medical Center
Vidio: What is Fuchs’ dystrophy? | Ohio State Medical Center

Fuchs (akpọrọ "fooks") dystrophy bụ ọrịa anya nke mkpụrụ ndụ na-etinye n'ime ime cornea ji nwayọ amalite ịnwụ. Ọrịa ahụ na-emetụtakarị anya abụọ.

Fuchs dystrophy nwere ike keta, nke pụtara na ọ nwere ike bufere nne na nna nye ụmụaka. Ọ bụrụ na nne na nna gị nwere ọrịa a, ị nwere ohere 50 nke ịmalite ọrịa ahụ.

Otú ọ dị, ọnọdụ ahụ nwekwara ike ịbịakwute ndị na-enweghị akụkọ ntolite ezinụlọ a maara nke ọrịa ahụ.

Fuchs dystrophy na-adịkarị na ụmụ nwanyị karịa ụmụ nwoke. Nsogbu ọhụụ anaghị apụta tupu afọ iri ise n'ọtụtụ oge. Otú ọ dị, onye nlekọta ahụike nwere ike ịhụ ihe ịrịba ama nke ọrịa ahụ na ndị metụtara site na 30s ma ọ bụ 40s.

Fuchs dystrophy na-emetụta ụyọkọ mkpụrụ ndụ nke dị n’azụ akụkụ nke cornea. Mkpụrụ ndụ ndị a na-enyere aka iwepụta oke mmiri nke cornea. Dika otutu sel na-efu, mmiri na-amalite ịba na cornea, na-eme ka ọzịza na cornea ojii.

Na mbu, mmiri nwere ike itolite naanị n’oge ụra, mgbe anya mechiri emechi. Ka ọrịa ahụ na-akawanye njọ, obere blisters nwere ike ịmalite. Ọfụma ahụ na-ebuwanye ibu ma mechaa daa. Nke a na-ebute anya mgbu. Fuchs dystrophy nwekwara ike ime ka ọdịdị nke cornea gbanwee, na-eduga n'ọtụtụ nsogbu ọhụụ.


Mgbaàmà nwere ike ịgụnye:

  • Anya mgbu
  • Anya na-enwu gbaa na ìhè
  • Foggy ma ọ bụ ọhụụ na-ahụ ụzọ, na nke mbụ naanị n'ụtụtụ
  • Coloredhụ ka agba halos gbara gburugburu ọkụ
  • Ọhụụ jọgburu onwe ya n'ụbọchị

Onye na-eweta ọrụ nwere ike ịchọpụta nsogbu Fuchs dystrophy n'oge ule oriọna.

Nyocha ndị ọzọ enwere ike ịme gụnyere:

  • Pachymetry - jikoro ọkpụrụkpụ nke cornea
  • Nyocha microscope zuru oke - na-enye ndị na-eweta ọrụ ohere ileba anya na obere mkpụrụ ndụ sel nke na-agbanye akụkụ azụ nke cornea
  • Nlere anya acuity

A na-eji anya mmiri ma ọ bụ mmanụ otite nke na-adọpụta mmiri site na cornea iji belata mgbaàmà nke Fuchs dystrophy.

Ọ bụrụ na ọnya na-egbu mgbu na-etolite na cornea, lenses kọntaktị dị nro ma ọ bụ ịwa ahụ iji mepụta ọnya na ọnyá nwere ike inye aka belata mgbu.

Nanị ọgwụgwọ maka Fuchs dystrophy bụ transplant corneal.

Ruo n'oge na-adịbeghị anya, ụdị ụdị nke corneal transplant na-abanye n'ime keratoplasty. N'oge usoro a, a na-ewepụ obere akụkụ nke cornea, na-ahapụ oghere n'ihu anya. A na-etinyezi cornea na-emekọ ihe site na onye nyere mmadụ aka n'ime oghere n'ihu anya.


Usoro ohuru a na-akpọ endothelial keratoplasty (DSEK, DSAEK, ma ọ bụ DMEK) aghọwo nhọrọ kachasị mma maka ndị nwere Fuchs dystrophy. N'ime usoro a, ọ bụ naanị akụkụ nke cornea ka edochiri, kama ọkwa niile. Nke a na - eduga na mgbake ngwangwa na obere nsogbu. Itdọ anaghị achọkarị.

Fuchs dystrophy na-akawanye njọ karịa oge. Na-enweghị ịkpụgharị ahụ, onye nwere oke Fuchs dystrophy nwere ike bụrụ onye ìsì ma ọ bụ nwee nnukwu ihe mgbu ma belata ọhụụ.

Ọnọdụ dị nro nke Fuchs dystrophy na-akawanye njọ mgbe a wachara ya. Onye dọkịta na-awa ahụ ga-enyocha ihe egwu a ma nwee ike gbanwee usoro ma ọ bụ oge ịwa ahụ gị.

Kpọọ onye na-ahụ maka ọrụ gị ma ọ bụrụ na ịnwee:

  • Anya mgbu
  • Anya na-enwu ìhè
  • Mmetụta na ihe dị gị n'anya mgbe ọ na-enweghị ihe ọ bụla
  • Ọhụụ ọhụụ dị ka ịhụ halos ma ọ bụ ọhụụ ojii
  • Ọhụụ jọgburu onwe ya

Enweghị mgbochi a maara. Izere ịwa ahụ gbasara ahụ ma ọ bụ ịkpachapụ anya pụrụ iche n’oge a na-awa ahụ nwere ike igbu oge maka ịkpụgharị corneal.


Fuchs ’dystrophy; Fuysts 'endothelial dystrophy; Fuchs 'corneal dystrophy nwere nsogbu

Folberg R. Anya. Na: Kumar V, Abbas AK, Aster JC, eds. Robbins & Cotran Pathologic Basis nke Ọrịa. Nke iri. Philadelphia, PA: Elsevier; 2021: Isi nke 29.

Chika Okpala N'ihe banyere ule na-adakarị na fuchs endothelial corneal dystrophy: nhazi ọkwa na nsonaazụ ya - Bowman Club Lecture 2019. BMJ Mepee Ophthalmology. 2019; 4 (1): E000321. PMID: 31414054 pubmed.ncbi.nlm.nih.gov/31414054/.

Rosado-Adames N, Afshari NA. Ọrịa nke corneal endothelium. Na: Yanoff M, Duker JS, eds. Ọrịa. Nke 5. Philadelphia, PA: Elsevier; 2019: isi 4.21.

Salmọn JF. Cornea. Na: Salmon JF, ed. Kanski’s Clinical Ophthalmology. Agba nke 9. Philadelphia, PA: Elsevier; 2020: isi 7.

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