Hemophilia

Hemophilia na-ezo aka na otu ọrịa ọgbụgba ọbara nke ọgbụgba ọbara na-ewe ogologo oge.

Dị abụọ nke hemophilia:

• Hemophilia A (kpochapụwo hemophilia, ma ọ bụ ihe na-akpata ụkọ nke asatọ)
• Hemophilia B (ọrịa Krismas, ma ọ bụ ihe kpatara IX)

Mgbe ị na-agba obara, usoro ihe na-eme n’ime ahụ nke na - enyere mkpụkọ ọbara aka. A na-akpọ usoro a coagulation cascade. Ọ gụnyere protein pụrụ iche a na-akpọ coagulation, ma ọ bụ ihe ndị na-eme ka ihe na-egbochi ọbara. Nwere ike ịnwe ohere dị elu nke ọbara ọgbụgba ma ọ bụrụ na otu ma ọ bụ karịa n'ime ihe ndị a na-efu ma ọ bụ na ha anaghị arụ ọrụ dịka ha kwesịrị.

Hemophilia na-ebute enweghị ihe mgbochi mkpokọta VIII ma ọ bụ IX na ọbara. N'ọtụtụ ọnọdụ, hemophilia na-agafe site na ezinụlọ (ketara). Ọtụtụ mgbe, ọ na-ebunye ya ụmụ nwoke.

Ihe mgbaàmà kachasị nke hemophilia bụ ọbara ọgbụgba. Enwere ike ịchọpụtaghị ikpe dị nro ruo mgbe ọ gasịrị na ndụ, mgbe ọhara nnukwu ọbara na-esote ịwa ahụ ma ọ bụ mmerụ ahụ.

N'ọnọdụ kachasị njọ, ọbara ọgbụgba na-eme n'enweghị ihe kpatara ya. Ọbara n'ime nwere ike ime ebe ọ bụla na ọbara ọgbụgba na nkwonkwo bụ ihe a na-ahụkarị.

Ọtụtụ mgbe, a na-achọpụta hemophilia mgbe mmadụ nwere nsogbu ọgbụgba na-adịghị mma. Enwere ike ịchọpụta ya site na nyocha ọbara emere iji chọpụta nsogbu ahụ, ma ọ bụrụ na ndị ọzọ nọ n'ezinụlọ nwere ọrịa ahụ.

Usoro ọgwụgwọ kachasịsịsịsị bụ iji dochie ihe na-efu mkpụkọ n'ime ọbara site na akwara (infusions intravenous).

Ekwesiri ilebara anya pụrụ iche n’oge ịwa ahụ ma ọ bụrụ na ị nwere ọrịa ọgbụgba a. Yabụ, jide n'aka na ịgwa dọkịta na-awa gị na ị nwere nsogbu a.

Ọ dịkwa ezigbo mkpa ịkọrọ ndị ikwu gị ihe gbasara ọrịa gị n'ihi na ha nwekwara ike metụta ya.

Banye n'òtù nkwado ebe ndị otu na-ekerịta otu okwu nwere ike belata nrụgide nke ọrịa ogologo oge (ọrịa).

Imirikiti ndị nwere hemophilia nwere ike ịme ihe nkịtị. Ma ụfọdụ ndị na-agbapụta ọbara n’ime nkwonkwo, nke nwere ike belata ọrụ ha.

Onu ogugu ndi mmadu hemophilia nwere ike nwuru nke nnukwu obara.

Hemophilia A; Omuma hemophilia; Ebumnuche VIII erughi; Hemophilia B; Ọrịa Christmas; Ihe kpatara IX erughi; Ọbara ọgbụgba - hemophilia

• Ọbara ọbara

Carcao M, Moorehead P, Lillicrap D. Hemophilia A na B. Na: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: ickpụrụ na Omume. Nke 7. Philadelphia, PA: Elsevier; 2018: isi 135.

JElọ Nzukọ JE. Hemostasis na coagulation ọbara. Na: JElọ Nzukọ JE, ed. Akwụkwọ Guyton na Halllọ Akwụkwọ Ahụike Ahụike. Nke 13. Philadelphia, PA: Elsevier; 2016: isi 37.

Ragni MV. Ọrịa ọgbụgba ọbara: ụkọ ihe kpatara nsogbu. Na: Goldman L, Schafer AI, eds. Ọgwụ Goldman-Cecil. Nke iri abụọ na ise. Philadelphia, PA: Elsevier Saunders; 2016: isi 174.