Otu esi agwọ mgbanwe nke ọrịa Beckwith-Wiedemann kpatara

Ndinaya

• Nchoputa nke ọrịa Beckwith-Wiedemann

Ọgwụgwọ maka ọrịa Beckwith-Wiedemann, nke bụ ọrịa na-adịghị ahụkebe congenital nke na-akpata njupụta nke akụkụ ụfọdụ nke ahụ ma ọ bụ akụkụ, dịgasị iche dịka mgbanwe nke ọrịa ahụ kpatara, ya mere, otu ndị na-eduzi ọgwụgwọ na-ejikarị ndị otu nwere ike ịgụnye pediatrician, cardiologist, dentist na ọtụtụ ndị dọkịta na-awa, dịka ọmụmaatụ.

Yabụ, dabere na mgbaàmà na nrụrụ nrụrụ kpatara ọrịa Beckwith-Wiedemann, ụdị usoro ọgwụgwọ bụ:

• Mbelata shuga shuga: injections nke ọbara na glucose na-eme kpọmkwem n'ime akwara na iji gbochie enweghi shuga na-akpata mgbanwe ngbanwe dị egwu;
• Ndibe ma obu inguinal hernias: ọgwụgwọ anaghị adịkarị mkpa ebe ọ bụ na ọtụtụ hernias na-apụ n'anya site na afọ mbụ nke ndụ, agbanyeghị, ọ bụrụ na hernia na-aga n'ihu na-abawanye na nha ma ọ bụ ọ bụrụ na ọ kwụsịghị ruo afọ 3, ọ nwere ike ịdị mkpa ịwa ahụ;
• Nnukwu asụsụ: enwere ike iji ịwa ahụ mee ihe iji dozie oke asụsụ ahụ, agbanyeghị, ekwesịrị ịme ya naanị mgbe afọ abụọ gachara. Ruo na afọ, i nwere ike iji ụfọdụ silicone nipples inyere nwa gị aka iri ihe n'ụzọ dị mfe karị;
• Nsogbu obi ma ọ bụ eriri afọ: a na-eji ọgwụ agwọ ụdị nsogbu ọ bụla, a ga-enwerịrị ya n'oge ndụ ya niile. N'okwu ndị kachasị njọ, dọkịta nwere ike ịkwado ịwa ahụ iji rụzie mgbanwe siri ike n'obi, dịka ọmụmaatụ.

Na mgbakwunye, ụmụaka amụrụ na ọrịa Beckwith-Wiedemann nwere ike nwee ọrịa kansa, yabụ ọ bụrụ na achọpụtara uto tumo, ọ nwekwara ike ịdị mkpa ịwa ahụ iji wepu mkpụrụ tumo ma ọ bụ ọgwụgwọ ndị ọzọ dị ka chemotherapy ma ọ bụ ọgwụgwọ radiation.

Kaosinadị, mgbe emechara ọgwụgwọ, ọtụtụ ụmụaka nwere ọrịa Beckwith-Wiedemann na-etolite n'ụzọ zuru oke, na-enweghị nsogbu n'oge okenye.

Nchoputa nke ọrịa Beckwith-Wiedemann

Nchoputa nke Beckwith-Wiedemann nwere ike ime site na ichoputa ihe ojoo mgbe amuchara nwa ma obu site na ule nyocha, dika ihe omimi abdominal, dika imaatu.

Na mgbakwunye, iji gosi nchoputa ahụ, dọkịta nwekwara ike ịnye nyocha ọbara ka o mee nyocha mkpụrụ ndụ ihe nketa ma chọpụta ma enwere mgbanwe na chromosome 11, ebe nke a bụ nsogbu mkpụrụ ndụ ihe nketa nke sitere na mmalite ọrịa ahụ.

Ọrịa Beckwith-Wiedemann nwere ike ibunye ndị nne na nna gaa na ụmụaka, yabụ ọ bụrụ na nne ma ọ bụ nna ọ bụla enweela ọrịa ahụ dịka nwatakịrị, a na-atụ aro ndụmọdụ gbasara mkpụrụ ndụ tupu ịtụrụ ime.