Ọrịa Fanconi

Ndinaya

• Mgbaàmà nke ọrịa ọrịa Fanconi
• Ọgwụgwọ ọrịa ọrịa Fanconi
• Bara uru njikọ:

Ọrịa Fanconi bụ ọrịa na-adịghị ahụkebe nke akụrụ nke na-eduga na nchịkọta glucose, bicarbonate, potassium, phosphates na ụfọdụ amino acid karịrị na mmamịrị. Na ọrịa a nwekwara oke protein na mmamịrị na mmamịrị na-esikwu ike ma bụrụ acidic.

Ihe nketa Fanconi Syndrome na-akpata mgbanwe mkpụrụ ndụ ihe nketa nke na-ebufe site n'aka nna na nwa nwoke. N'okwu nke Ọrịa Fanconi nwetara, ingestion of metal arọ, dị ka ụzọ, ingestion nke ọgwụ nje kubie ume, ụkọ vitamin D, akụrụ transplantation, ọtụtụ myeloma ma ọ bụ amyloidosis nwere ike ibute mmepe nke ọrịa ahụ.

Ọrịa Fanconi enweghị ọgwụgwọ na ọgwụgwọ ya gụnyere tumadi ị dochie ihe ndị mmamịrị furu efu, nke ọkà mmụta nephrologist gosipụtara.

Mgbaàmà nke ọrịa ọrịa Fanconi

Ihe mgbaàmà nke ọrịa Fanconi nwere ike ịbụ:

• Urinụ nnukwu mmamịrị;
• Mmiri na mmiri siri ike;
• Akpịrị kpọrọ nkụ;
• Akpịrị ịkpọ nkụ;
• Obere;
• Nnukwu acidity n’ime ọbara;
• Adịghị ike;
• Ọkpụkpụ mgbu;
• Kọfị-mmiri ara agba patch ke ikpa;
• Enweghị ma ọ bụ nkwarụ na mkpịsị aka;

N'ozuzu, njirimara Fanconi Syndrome ihe nketa na-apụta na nwata n’ihe dị ka afọ 5.

O nchoputa nke oria Fanconi a na-eme ya dabere na mgbaàmà ahụ, ule ọbara nke na-ekpughe nnukwu acidity na ule mmamịrị nke na-egosi oke glucose, phosphate, bicarbonate, uric acid, potassium na sodium.

Ọgwụgwọ ọrịa ọrịa Fanconi

Ọgwụgwọ Syndrome Fanconi chọrọ iji gbakwunye bekee ndị mmadụ na mamịrị tufuru. Maka nke a, ọ nwere ike ịdị mkpa ka ndị ọrịa were potassium, phosphate na vitamin D supplementation, yana sodium bicarbonate iji belata ọbara acidosis.

Na ndị ọrịa nwere nnukwu ntụpọ akụrụ, egosiputa transplantation akụrụ.

Bara uru njikọ:

• Nri nwere ọgaranya
• Nri bara ọgaranya na vitamin D

• Akụrụ Akụrụ