Nnwale Porphyrin

Ndinaya

• Kedu ihe bụ porphyrin tests?
• Kedu ihe eji ha eme?
• Gịnị kpatara m ji chọọ ule porphyrin?
• Kedu ihe na-eme n'oge ule porphyrin?
• Ọ dị m mkpa ime ihe ọ bụla iji kwadebe maka ule ahụ?
• Onwere ihe egwu di na porphyrin ule?
• Kedu ihe nsonaazụ ahụ pụtara?
• Onwere ihe ozo ichoro ima banyere porphyrin tests?
• Ntughari

Kedu ihe bụ porphyrin tests?

Nnyocha Porphyrin na-atụle ogo nke porphyrins n'ọbara gị, mmamịrị, ma ọ bụ stool gị. Porphyrins bụ kemịkalụ nke na - enyere aka haemoglobin, ụdị protein na mkpụrụ ndụ ọbara uhie gị. Hemoglobin na-ekunye oxygen site n’akpa ume gị n’akụkụ ahụ́ gị ndị ọzọ.

Ọ bụ ihe kwesịrị ekwesị inwe obere porphyrins n’ọbara gị na mmiri ahụ ndị ọzọ. Ma oke inye aka nwere ike ịpụta na ị nwere ụdị nke porphyria. Porphyria bụ ọrịa na-adịghị ahụkebe nke nwere ike ibute nnukwu nsogbu ahụike. A na - ekewa Porphyria ụzọ abụọ:

• Nnukwu porphyrias, nke kachasị emetụta usoro ụjọ ahụ na-ebute mgbaàmà afọ
• Cutaneous porphyrias, nke na-akpata mgbaàmà anụ ahụ mgbe ìhè anyanwụ na-acha gị

Porfọdụ porphyrias na-emetụta ma usoro ụjọ ahụ na anụ ahụ.

Aha ndị ọzọ: protoporphyrin; protoporphyrin, ọbara; protoporhyrin, oche; porphyrins, nsị; uroporphyrin; porphyrins, mmamịrị; Nwale Mauzerall-Granick; acid; ALA; porphobilinogen; PBG; free erythrocyte protoporphyrin; ẹphe erythrocyte porphyrins; FEP

Kedu ihe eji ha eme?

A na-eji ule Porphyrin achọpụta ma ọ bụ nyochaa porphyria.

Gịnị kpatara m ji chọọ ule porphyrin?

Nwere ike ịchọ nyocha porphyrin ma ọ bụrụ na ị nwere mgbaàmà nke porphyria. E nwere ihe mgbaàmà dị iche maka ụdị porphyria dị iche iche.

Mgbaàmà nke nnukwu porphyria gụnyere:

• Ime mgbu
• Afọ ntachi
• Ọgbọ na ọgbụgbọ
• Uhie na-acha uhie uhie ma ọ bụ nchara nchara
• Ntughari ma ọ bụ ihe mgbu aka na / ma ọ bụ ụkwụ
• Ike adịghị ike
• Mgbagha
• Nnukwu ihe

Mgbaàmà nke ọnyá porphyria gụnyere:

• Nlebara anya na ìhè anyanwụ
• Iberibe ọnya na akpụkpọ gụrụ ìhè anyanwụ
• Na-acha uhie uhie na ọzịza na anụ ahụ ekpughere
• Itching
• Mgbanwe na agba akpụkpọ

Nwekwara ike ịchọ ule porphyrin ma ọ bụrụ na onye ezinụlọ gị nwere porphyria. Ọtụtụ ụdị porphyria na-eketa, nke pụtara na ọnọdụ ahụ si na nne na nna gafere nwa.

Kedu ihe na-eme n'oge ule porphyrin?

Enwere ike ịnwale Porphyrins na ọbara, mmamịrị, ma ọ bụ stool. E depụtara ụdị ụdị porphyrin ndị a n'okpuru.

• Nnwale ọbara
  • Onye ọkachamara ahụike ga-ewere ihe nyocha ọbara site na akwara aka gị, jiri obere agịga. Mgbe etinyere agịga ahụ, a ga-achịkọta obere ọbara n'ime ule nyocha ma ọ bụ vial. Nwere ike na-eche ntakịrị ihe mgbe agịga na-abanye ma ọ bụ na-apụta. Nke a na-ewe ihe na-erughị nkeji ise.
• 24-Hour Akwụkwọ mmamịrị
  • Ga-anakọta mmamịrị gị niile n'oge oge 24. Maka ule a, onye nlekọta ahụike gị ma ọ bụ ụlọ nyocha ga-enye gị akpa na ntuziaka akọwapụtara banyere otu esi anakọta ihe nlele gị n'ụlọ. Jide n'aka na ị gbasoro ntuziaka niile nke ọma. A na-eji ule mmamịrị a na-arụ ọrụ elekere 24 n'ihi na ọtụtụ ihe dị na mmamịrị, gụnyere porphyrin, nwere ike ịdị iche na ụbọchị niile. Ya mere ichikota otutu ihe nlebara anya n’otu ubochi nwere ike inye nkowa zuru oke banyere ihe mmamiri gi.
• Nnwale Uzo Ozo
  • Can nwere ike ịnye ihe nlele gị n'oge ọ bụla nke ụbọchị, na-enweghị nkwadebe pụrụ iche ma ọ bụ njikwa dị mkpa. Ule a na-emekarị na ụlọ ọrụ nlekọta ahụike ma ọ bụ ụlọ nyocha.
• Nnwale oche (nke a na-akpọ protoporphyrin na stool)
  • Ga-anakọta ala oche gị ma tinye ya na igbe pụrụ iche. Onye na - ahụ maka ahụike gị ga - enye gị ntụzịaka etu ị ga - esi kwadebe ihe nlele gị ma ziga ya lab.

Ọ dị m mkpa ime ihe ọ bụla iji kwadebe maka ule ahụ?

Don’tkwesighi nkwadebe pụrụ iche maka ọbara ma ọ bụ mmamịrị nyocha.

Maka ule stool, enwere ike ịgwa gị ka ị ghara iri anụ ma ọ bụ were ọgwụ ọ bụla nwere ọgwụ aspirin ruo ụbọchị atọ tupu ule gị.

Onwere ihe egwu di na porphyrin ule?

O nwechaghị ihe egwu dị n’inyocha ọbara. May nwere ike ịnwe obere ihe mgbu ma ọ bụ mmerụ ahụ ebe etinyere agịga ahụ, mana ọtụtụ mgbaàmà na-apụ ngwa ngwa.

Onweghi ihe onodu a matara na mmamiri ma obu stool.

Kedu ihe nsonaazụ ahụ pụtara?

Ọ bụrụ na ahụrụ nnukwu porphyrin n’ọbara gị, mamịrị gị, ma ọ bụ n’elu oche gị, onye na-ahụ maka ahụike gị nwere ike ịgwa ndị ọzọ ule iji gosi nchoputa na ịchọpụta ụdị porphyria ị nwere. Ọ bụ ezie na enweghị ọgwụgwọ maka porphyria, enwere ike ijikwa ọnọdụ ahụ. Changesfọdụ mgbanwe ndụ na / ma ọ bụ ọgwụ nwere ike inye aka gbochie mgbaàmà na nsogbu nke ọrịa ahụ. Specific ọgwụgwọ na-adabere na ụdị porphyria i nwere. Ọ bụrụ na ị nwere ajụjụ gbasara nsonaazụ gị ma ọ bụ gbasara porphyria, gwa ndị na-elekọta ahụike gị.

Mụtakwuo maka ule nyocha ụlọ, akara ngosi, na nghọta nsonaazụ.

Onwere ihe ozo ichoro ima banyere porphyrin tests?

Ọ bụ ezie na ọtụtụ ụdị porphyria na-eketa, ụdị ndị ọzọ porphyria nwekwara ike nweta. Enwere ike ị nweta porphyria site n'ọtụtụ ihe, gụnyere ị oụbiga mmanya ókè, HIV, ịba ọcha n'anya C, ị ironụbiga ihe ike, na / ma ọ bụ ị alcoholụbiga mmanya ókè.

Ntughari

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Ejila ozi dị na saịtị a dị ka onye dochie anya nlekọta ahụike ọkachamara ma ọ bụ ndụmọdụ. Kpọtụrụ onye na-ahụ maka ahụike ma ọ bụrụ na ị nwere ajụjụ gbasara ahụike gị.