Anomalous hapụrụ akwara akwara si akpa ume

Anomalous ekpe akwara akwara si akpa ume akwara (ALCAPA) bụ obi nkwarụ. Akwara akwara ọbara aka ekpe (LCA), nke na-eburu ọbara na akwara obi, na-amalite site na akwara pulmonary kama aorta.

ALCAPA dị na mgbe a mụrụ ya (congenital).

ALCAPA bụ nsogbu na - eme mgbe mkpụrụ obi nwata na - amalite n’oge afọ ime. Akụkụ ọbara nke na - etolite n’akwara obi anaghị ekekọta n’ụzọ ziri ezi.

N'ime obi nkịtị, LCA sitere na aorta. Ọ na-enye ọbara akụrụngwa oxygen na akwara obi n'akụkụ aka ekpe nke obi yana mitral valve (valvụ obi n'etiti etiti ụlọ elu na nke ala nke obi n'akụkụ aka ekpe). Aorta bụ arịa buru ibu nke na-ewe ọbara oxygen na-esi n’obi sitere n’akụkụ ahụ nke ọzọ.

N'ime ụmụaka nwere ALCAPA, LCA sitere na akwara akpa ume. Ọbara akpa ume bụ nnukwu arịa ọbara nke na-eburu ọbara oxygen-adịghị mma sitere na obi gaa n'akpa ume iji bulie oxygen.

Mgbe nkwarụ a pụtara, a na-ebute ọbara na-enweghị oxygen na akwara obi n'akụkụ aka ekpe nke obi. Ya mere, akwara obi anaghị enweta oxygen zuru oke. Anụ ahụ na-amalite ịnwụ n'ihi enweghị oxygen. Nke a nwere ike ịkpata nkụchi obi na nwa ahụ.

Ọnọdụ a maara dị ka "akwara ọbara" na-emebi obi n'obi ụmụ ọhụrụ nwere ALCAPA. Ọbara dị ala nke na-eme ka ọbara ọgbụgba na-eme ka ọbara sitere na LCA jikọtara ya ka ọ laghachi azụ na akwara pulmonary kama ịga akwara obi. Nke a na - ebute ọbara na ikuku oxygen na akwara obi. Nsogbu a nwekwara ike ibute ọrịa obi na nwa. Coronary ohi na-amalite n'oge na ụmụ ọhụrụ nwere ALCAPA ma ọ bụrụ na agwọghị ọnọdụ ahụ n'oge.

Mgbaàmà nke ALCAPA na nwa ọhụrụ gụnyere:

• Ibe ákwá ma ọ bụ ọsụsọ n’oge nri
• Iwe
• Icha akpụkpọ
• Ogbenye nri
• Na-eku ume ngwa ngwa
• Mgbaàmà nke mgbu ma ọ bụ nhụjuanya na nwa (na-ezighi ezi na colic)

Mgbaàmà nwere ike ịpụta n’ime ọnwa abụọ mbụ nke ndụ nwa ahụ.

Dịka, a na-achọpụta ALCAPA n'oge ọ bụ nwa ọhụrụ. N'ọnọdụ ndị na-adịkarị, a naghị achọpụta ntụpọ a ruo mgbe mmadụ bụ nwata ma ọ bụ okenye.

N'oge ule, onye nlekọta ahụike ga-ahụ ihe ịrịba ama nke ALCAPA, gụnyere:

• Uche ndi ozo
• Ibawanye obi
• Obi ntamu (obere)
• Otutu usu

Ule ndị a pụrụ inye iwu gụnyere:

• Echocardiogram, nke bu ultrasound nke n’ahu obi obi na obara obara n’ime obi
• Electrocardiogram (ECG), nke na-atụle ọrụ eletriki nke obi
• Igbe x-ray
• MRI, nke na-enye nkọwa zuru ezu nke obi
• Cardiac catheterization, a usoro nke a mkpa tube (catheter) na-etinye n'ime obi na-ahụ na-eruba ọbara na-ewere ezi nha nke ọbara mgbali na oxygen etoju

Gerywa ahụ dị mkpa iji dozie ALCAPA. Naanị otu ịwa ahụ dị mkpa n'ọtụtụ ọnọdụ. Otú ọ dị, ịwa ahụ ga-adabere na ọnọdụ nwa ahụ na oke nke arịa ọbara metụtara.

Ọ bụrụ na akwara obi na-akwado mitral valvụ mebiri emebi site na ikuku oxygen na-ebelata, nwa ahụ nwekwara ike chọọ ịwa ahụ iji mezie ma ọ bụ dochie valvụ ahụ. Mkpụrụ mitral ahụ na-achịkwa ọbara na-eru n'etiti ụlọ dị n'akụkụ aka ekpe nke obi.

Enwere ike ime ihe ntụgharị obi ma ọ bụrụ na obi nwa ahụ mebiri emebi n'ihi enweghị oxygen.

Ọgwụ eji gụnyere:

• Mkpụrụ mmiri (mamịrị)
• Ọgwụ nke na-eme ka akwara obi nwee ume ike (ndị ọrụ inotropic)
• Ọgwụ nke na-agbadata ibu ọrụ na obi (beta-blockers, ACE inhibitors)

Enweghị ọgwụgwọ, ọtụtụ ụmụ ọhụrụ anaghị adị ndụ n'afọ mbụ ha. Childrenmụaka ndị lanarịrị na-enweghị ọgwụgwọ nwere ike ịnwe nnukwu nsogbu obi. Mụaka nwere nsogbu a anaghị agwọ ọrịa nwere ike ịnwụ na mberede n’afọ ndị sochirinụ.

Na ọgwụgwọ oge mbụ dịka ịwa ahụ, ọtụtụ ụmụ ọhụrụ na-eme nke ọma ma nwee ike ịtụ anya ndụ dị mma. A ga-achọ ndị na-esochi oge na ọkachamara n'ọkachamara obi (cardiologist).

Nsogbu nke ALCAPA gụnyere:

• Obi nkolopu
• Obi mgbawa
• Nsogbu obi
• Na-adịgide na-emebi obi

Kpọọ onye na-eweta gị ma ọ bụrụ na nwa gị:

• Na-eku ume ngwa ngwa
• O yiri ka icha mmirimmiri
• O yiri ka obi erughị ala ma na-ebe ákwá mgbe mgbe

Anomalous si n'aka ekpe akwara akwara na-esite n'akwara akpa ume; ALCAPA; Ọrịa ALCAPA; Ọrịa Bland-White-Garland; Ọrịa congenital - ALCAPA; Omumu omumu - ALCAPA

• Anomalous hapụrụ akwara akwara

Jmụnna JA, Frommelt MA, Jaquiss RDB, Myerburg RJ, Fraser CD Jr, Tweddell JS. Ndị ọkachamara na-ekwenye na nkwenye: mmalite aortic sitere na akwara obi. J Thorac Cardiovasc Surg. Ọrịa. 2017; 153 (6): 1440-1457. PMID: 28274557 pubmed.ncbi.nlm.nih.gov/28274557/.

Jmụnna JA, Gaynor JW. Wa ahụ maka ọrịa na-efe efe nke akwara obi. Na: Sellke FW, del Nido PJ, Swanson SJ, eds. Istwa Ahụ Sabiston na Spencer nke Obi. Agba nke 9. Philadelphia, PA: Elsevier; 2016: isi 124.

Johnson JT, Harris M, Anderson RH, Spicer DE, Jacobs M, Tweddll JS, et al. Naịjirịa Congenital akwara anomalies. Na: Wernovsky G, Anderson RH, Kumar K, et al. Anderson’s Ọrịa edimụaka Cardiology. Agba nke anọ. Philadelphia, PA: Elsevier; 2020: isi 46.

Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM. Obi ndi ozo na obi ojoo. Na: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Akwụkwọ ọgụgụ nke Ọrịa edimụaka. 21nke. Philadelphia, PA: Elsevier; 2020: isi 459.