Ogwu

Cystinuria bụ ọnọdụ na - adịghị ahụkebe nke nkume sitere na amino acid akpọrọ cysteine ​​n'ụdị akụrụ, ureter, na eriri afo. A na-akpụ Cystine mgbe mkpụrụ ndụ abụọ nke amino acid a na-akpọ cysteine ​​jikọtara ọnụ. Ọnọdụ a gafere ezinụlọ.

Iji nweta ihe mgbaàmà nke cystinuria, ị ga-eketa usoro na-ezighi ezi site n'aka nne na nna. Yourmụ gị ga-enwetakwa otu mkpụrụ ndụ ihe nketa na-ezighi ezi n'aka gị.

A na-akpata cystinuria site na oke cystine na mmamịrị. Dị ka ọ dị, ọtụtụ cystine na-agbaze ma laghachi n'ọbara mgbe ha banyere akụrụ. Ndị nwere cystinuria nwere nkwarụ mkpụrụ ndụ ihe nketa nke na-egbochi usoro a. N'ihi ya, cystine na-amalite na mmamịrị ma na-akpụ kristal ma ọ bụ nkume. A kristal ndị a nwere ike ịrabanye na akụrụ, ureters, ma ọ bụ eriri afo.

Ihe dị ka otu onye n’ime mmadụ asaa ọ bụla nwere cystinuria. Nkume cystine na-akachasị eto eto na ndị na-eto eto nọ n'okpuru afọ 40. Ihe na-erughị 3% nkume urinary bụ nkume cystine.

Mgbaàmà gụnyere:

• Ọbara na mmamịrị
• Ahụ mgbu ma ọ bụ ihe mgbu n'akụkụ ma ọ bụ azụ. Mgbu na-abụkarị otu akụkụ. A naghị enwekarị mmetụta n'akụkụ abụọ. Mgbu na-adịkarị njọ. O nwere ike ịka njọ ụbọchị. I nwekwara ike inwe ihe mgbu na pelvis, ukwu, akụkụ ahụ nwoke ma ọ bụ nwaanyị, ma ọ bụ n’agbata afọ elu na azụ.

A na-ahụkarị ọnọdụ ahụ mgbe ihe omume nke akụrụ akụrụ. Inwale nkume mgbe ewepụchara ha na-egosi na ọ bụ nke cystine.

N'adịghị ka nkume ndị nwere calcium, nkume cystine adịghị egosipụta nke ọma na ụzarị ọkụ.

Ule nwere ike ime iji chọpụta nkume ndị a ma chọpụta ọnọdụ ahụ gụnyere:

• 24-awa mmamịrị collection
• Ime CT scan, ma ọ bụ ultrasound
• Pralogram igba ogwu (IVP)
• Urinalysis

Ebumnuche nke ọgwụgwọ bụ iji belata mgbaàmà ma gbochie ọtụtụ nkume ịmalite. Onye nwere nnukwu mgbaàmà kwesịrị ịga ụlọ ọgwụ.

Ọgwụgwọ gụnyere ị drinkingụ ọtụtụ mmiri, ọkachasị mmiri, iji mepụta nnukwu mmamịrị. I kwesiri ị drinkụ ma ọ dịkarịa ala iko isii ruo 8 kwa ụbọchị. Should kwesịrị ị drinkụ mmiri n'abalị ka ị bilie n'abalị ọ dịkarịa ala otu oge iji gbanye mamịrị.

N'ọnọdụ ụfọdụ, mmiri nwere ike ịdị mkpa site na akwara (site na IV).

Ime mmamịrị ahụ karịa alkaline nwere ike inyere aka igbari kristal cystine. Enwere ike ime nke a site na iji potassium citrate ma ọ bụ sodium bicarbonate. Iri obere nnu nwekwara ike ibelata ntọhapụ cystine na nguzobe okwute.

Nwere ike ịchọ ihe mgbatị iji chịkwaa ihe mgbu na akụrụ ma ọ bụ eriri afo ebe ị gafere nkume. Okwute pere mpe (nke dị 5 mm ma ọ bụ ihe na-erughị 5 mm) na-esikarị na ya agafe mmamịrị ahụ. Nkume buru ibu (ihe karịrị 5 mm) nwere ike ịchọ ọgwụgwọ ọzọ. Largefọdụ nnukwu okwute nwere ike ịdị mkpa iji wepụ usoro iji:

• Extracorporeal shock wave lithotripsy (ESWL): A na-ebugharị ebili mmiri site na ozu ma lekwasị anya na okwute iji kewaa ya n'ime obere iberibe mpempe. ESWL nwere ike ọ gaghị arụ ọrụ nke ọma maka nkume cystine n'ihi na ha siri ike ma e jiri ya tụnyere ụdị nkume ndị ọzọ.
• Percutaneous nephrostolithotomy ma ọ bụ nephrolithotomy: A na-etinye obere ọkpọkọ n'akụkụ akụkụ ahụ kpọmkwem na akụrụ. A na-ejizi onyokomita agafee n’ime tube ahụ iji kewaa okwute n’okpuru ọhụụ.
• Ureteroscopy na laser lithotripsy: A na-eji laser agbaji nkume ma nwee ike iji ya na-agwọ nkume ndị na-adịchaghị oke.

Cystinuria bụ adịghị ala ala, ndụ niile. Okwute na-alọghachi. Otú ọ dị, ọnọdụ ahụ adịkarịghị akpata ọdịda akụrụ. Ọ naghị emetụta akụkụ ndị ọzọ.

Nsogbu nwere ike ịgụnye:

• Eriri afo mmerụ si nkume
• Akụrụ mmerụ si nkume
• Akụrụ ọrịa
• Ọrịa akụrụ na-adịghị ala ala
• Urepu mgbochi
• Urinary tract ọrịa

Kpọọ onye na-ahụ maka ahụike gị ma ọ bụrụ na ị nwere mgbaàmà nke nkume urinary tract.

Enwere ọgwụ enwere ike ị soụ ya ka cystine anaghị eme okwute. Jụọ onye na-enye gị ọrụ gbasara ọgwụ ndị a na ọghọm ha.

Onye ọ bụla nwere akụkọ ihe mere eme banyere nkume n'ime urinary tract kwesịrị ị drinkụ ọtụtụ mmiri mmiri iji mepụta nnukwu mmamịrị mgbe niile. Nke a na-eme ka okwute na kristal nwee ike ịhapụ ahụ tupu ha buru oke ibu iji bute mgbaàmà. Belata nnu gị ma ọ bụ sodium ga-enyere aka.

Nkume - cystine; Nkume Cystine

• Nkume akụrụ na lithotripsy - nhapu
• Nkume akụrụ - nlekọta onwe gị
• Nkume akụrụ - ihe ị ga-ajụ dọkịta gị
• Usoro urinary percutaneous - ihapu

• Nwanyi urinary tract
• Nwoke urinary tract
• Ogwu
• Nephrolithiasis

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Guay-Woodford LM. Ihe nketa nephropathies na enweghi nsogbu nke urinary tract. Na: Goldman L, Schafer AI, eds. Ọgwụ Goldman-Cecil. Nke 26th. Philadelphia, PA: Elsevier; 2020: isi 119.

Lipkin ME, Ferrandino MN, Na-eme GM. Nyocha na njikwa ahụike nke urinary lithiasis. Na: Wein AJ, Kavoussi LR, Partin AW, Peters CA, eds. Ulology nke Campbell-Walsh. Nke 11. Philadelphia, PA: Elsevier; 2016: isi 52.

Sakhaee K, Moe OW. Urolithiasis. Na: Yu ASL, Chertow GM, Luyckx VA, Marsden PA, Skorecki K, Taal MW, eds. Brenner na Rector nke akụrụ. Nke 11. Philadelphia, PA: Elsevier; 2020: isi 38.