Ugboro abụọ nri ụzọ

Ugboro abuo nke uzo nri (DORV) bu oria obi nke na adi site na nwa (congenital). Aorta na - ejikọ aka na ventricle aka nri (RV, ọnụ ụlọ nke obi nke na - atụba ọbara oxygen na - enweghị ume na ngụgụ), kama n'akụkụ aka ekpe (LV, ụlọ nke na - ewepụta ọbara nwere oxygen na ahụ).

Ma akwara pulmonary (nke na-eburu ọbara na-enweghị oxygen na ngụgụ) na aorta (nke na-ebu ọbara oxygen na-esi n'obi na anụ ahụ) si n'otu ụlọ mgbapụta. Ọ dịghị akwara jikọtara na ventricle aka ekpe (ụlọ ahụ na-agbanye ọbara na ahụ).

N'ime usoro obi nkịtị, akwara na-ejikọ na LV. Akwara akpa ume ejikọrọ na RV. Na DORV, akwara abụọ na-esite na RV. Nke a bụ nsogbu n'ihi na RV na-ebu ọbara oxygen-ogbenye. Ọbara a na-agagharịzi n’ahụ niile.

Mmetụta ọzọ a na-akpọ ntụpọ ventricular septal ntụpọ (VSD) na-apụta mgbe niile na DORV.

Ọbara oxygen bara ụba na ngụgụ na-esi n'akụkụ aka ekpe nke obi na-aga, site na mmeghe VSD na n'ime RV. Nke a na - enyere nwata aka nwere DORV site na ikwe ka ọbara oxygen nwere ọgwakọta ya na ọbara oxygen. Ọbụna na ngwakọta a, ahụ nwere ike ọ gaghị enweta ezigbo oxygen. Nke a na-eme ka obi na-arụ ọrụ nke ọma iji gboo mkpa ahụ. E nwere ọtụtụ ụdị DORV.

Ihe dị iche n'etiti ụdị ndị a bụ ọnọdụ nke VSD ebe ọ metụtara ọnọdụ nke akpa ume na aorta. Ihe mgbaàmà ya na oke nsogbu a ga-adabere n'ụdị DORV. Ọnụnọ nke eriri akpa ume na-emetụtakwa ọnọdụ ahụ.

Ndị nwere DORV na-enwekarị ntụpọ obi ndị ọzọ, dịka:

• Nkwarụ ikuku nke endocardial (mgbidi na-ekewa ụlọ anọ nke obi adịghị mma ma ọ bụ na-anọghị)
• Coarctation nke aorta (ibelata aorta)
• Nsogbu valve mitral
• Pulmonary atresia (akpa ume akpapụghị nke ọma)
• Pulmonary valve stenosis (ibelata nke akpa ume akpa ume)
• Ogwe aka akuku aka nri (akuku aortic di n'aka nri kama aka ekpe)
• Nnukwu usoro akwara (akwara na akpa ume na-agbanye)

Ihe ịrịba ama nke DORV nwere ike ịgụnye:

• Ibawanye obi
• Obi na-atamu ntamu
• Na-eku ume ngwa ngwa
• Otito otiti

Mgbaàmà nke DORV nwere ike ịgụnye:

• Nri na-adịghị mma site na ike ọgwụgwụ
• Akpụkpọ anụ na egbugbere ọnụ Bluish
• Mkpịsị ụkwụ (ndim nke akwa ntu) nke mkpịsị ụkwụ na mkpịsị aka (akara aka)
• Enweghị ike iburu ibu ma too
• Icha agba
• Sụsọ
• Fụrụ akpụ ụkwụ ma ọ bụ afọ
• Nsogbu iku ume

Ule iji chọpụta DORV gụnyere:

• Igwe ụzarị
• Nyocha nke Ultrasound nke obi (echocardiogram)
• Gafe tube dị gịrịgịrị, na-agbanwe agbanwe n'ime obi iji tụọ ọbara mgbali elu ma gbanye akwa maka foto pụrụ iche nke obi na akwara.
• Obi MRI

Ọgwụgwọ chọrọ ịwa ahụ iji mechie oghere n'ime obi ma tinye ọbara site na ventricle aka ekpe gaa na aorta. Ọwa nwere ike ịdị mkpa iji bugharịa akpa ume ma ọ bụ akwara.

Ihe ndị na - ekpebi ụdị na ọnụọgụ ọrụ nwata ahụ chọrọ gụnyere:

• Ofdị DORV
• Ogo nke ntụpọ ahụ
• Ọnụnọ nke nsogbu ndị ọzọ dị n'obi
• Ọnọdụ nwatakịrị ahụ dum

Otu nwa si eme nke ọma dabere na:

• Nha na ọnọdụ nke VSD
• Ogo nke ụlọ ndị na-agbapụta agba
• Ọnọdụ nke aorta na akpa ume
• Ọnụnọ nke nsogbu ndị ọzọ (dịka coarctation nke aorta na mitral valve nsogbu)
• Ahụike nwa ahụ dum n’oge nyocha
• Ma mmebi ngụgụ emeela site n'ọbara buru oke ibu na-aga n'akpa ume ogologo oge

Nsogbu sitere na DORV nwere ike ịgụnye:

• Obi mgbawa
• Ọbara mgbali elu dị na ngụgụ, nke enweghị ọgwụgwọ nwere ike ibute mmebi ngụgụ na-adịgide adịgide
• Ọnwụ

Childrenmụaka nwere ọnọdụ obi a nwere ike chọọ ị toụ ọgwụ nje tupu ọgwụgwọ eze. Nke a na-egbochi ịrịa ọrịa gburugburu obi. A pụkwara ịchọ ọgwụ nje mgbe a wachara gị ahụ.

Kpọọ onye na-ahụ maka ahụike gị ma nwa gị yie ka ike agwụ ya ngwa ngwa, nsogbu na-eku ume, ma ọ bụ nwee anụahụ ma ọ bụ egbugbere ọnụ. Ikwesiri ịjụ onye na-eweta gị ma ọ bụrụ na nwa gị anaghị eto eto ma ọ bụ na-ebu ibu.

DORV; Taussig-Bing anomaly; DORV na VSD gbara mbọ ugboro abụọ; DORV nwere VSD noncommit; DORV nwere subaortic VSD; Ọrịa obi congenital - DORV; Obi obi Cyanotic - DORV; Omumu omumu - DORV

• Ugboro abụọ nri ụzọ

Bichell D. Ogwe aka nri abụọ. Na: Ungerleider RM, Meliones JN, McMillian KN, Cooper DS, Jacobs JP, eds. Ọrịa Obi Ọjọọ na Infmụaka na Childrenmụaka. Nke atọ ed. Philadelphia, PA: Elsevier; 2019: isi 58.

Haller C, Van Arsdell GS, Yoo SJ, George-Hyslop CST, Spicer DE, Anderson A. Ugboro abụọ. Na: Wernovsky G, Anderson RH, Kumar K, et al. Anderson’s Ọrịa edimụaka Cardiology. Agba nke anọ. Philadelphia, PA: Elsevier; 2020: isi 39.

Webb GD, Smallhorn JF, Therrien J, Redington AN. Congenital ọrịa obi na okenye na ụmụaka na-enwe ndidi. Na: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. Ọrịa Obi Braunwald: Akwụkwọ ọgụgụ nke Ọgwụ Ọrịa Cardiovascular. Nke 11. Philadelphia, PA: Elsevier; 2019: isi 75.