Odee: Joan Hall
OfbọChị Okike: 6 Februari 2021
DatebọChị Mmelite: 16 Onwa Epurel 2025
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Ihe nyocha nke VIII bụ nyocha ọbara iji tụọ ọrụ nke ihe nke Asatọ. Nke a bụ otu n’ime protein ndị dị n’ime ahụ nke na-enyere aka ịgbanye ọbara.

Achọrọ nlebara ọbara.

Enweghị mkpa pụrụ iche.

Mgbe etinyere agịga ahụ iji see ọbara, ụfọdụ ndị na-enwe oke mgbu. Ndị ọzọ na-eche nanị ịpị ma ọ bụ gbaa. Mgbe nke ahụ gasịrị, enwere ike ịpị ụfọdụ ụtarị ma ọ bụ ọnyá ntakịrị. Nke a ga - apụ n'anya.

A na-eji ule a chọpụta ihe kpatara ọbara ọgbụgba (mgbatị ọbara na-ebelata). Ma obu, enwere ike inye ya iwu ma oburu na onye ezinaulo amara na ha nwere hemophilia A. A ga-emekwa ule a ka o wee hu otu ogwu ogwu hemophilia A si aru oru.

A nkịtị uru bụ 50% na 200% nke laabu akara ma ọ bụ akwụkwọ uru.

Usoro ntanetị dị iche iche nwere ike ịdịtụ iche n'etiti ụlọ nyocha dị iche iche. Lafọdụ labs na-eji nha dị iche iche ma ọ bụ nwee ike nwalee ụdị dị iche iche. Gwa onye na - enye gi ahu ike banyere ihe nlere gi putara.

Mbelata ihe nke VIII ọrụ nwere ike ịbụ n'ihi:


  • Hemophilia A (ọrịa ọgbụgba nke kpatara ọbara ọgbụgba nke asatọ)
  • Ọrịa nke ndị na-edozi ahụ nke na-achịkwa nsị ọbara na-arụ ọrụ na-ekesa coagulation intravascular (DIC)
  • Ọnụnọ nke ihe na-akpata VIII inhibitor (antibody)
  • Ọrịa Von Willebrand (ụdị ọrịa ọgbụgba ọzọ)

Ọrụ ka ukwuu nwere ike ịbụ n'ihi:

  • Erka nká
  • Ọrịa shuga
  • Ọrịa imeju
  • Mbufụt
  • Ime afọ ime
  • Ibu

E nwere obere ihe ize ndụ gụnyere ịnara ọbara gị. Akwara na akwara na-adị iche na nha site na otu onye gaa na onye ọzọ, na site n'otu akụkụ nke ahụ gaa na nke ọzọ. Samplenata ọbara ọbara nke ụfọdụ ndị mmadụ nwere ike isi ike karịa n'aka ndị ọzọ.

Ihe ize ndụ ndị ọzọ metụtara ịmịnye ọbara dị ntakịrị, mana nwere ike ịgụnye:

  • Ọbara ọgbụgba
  • Da mba ma ọ bụ inwe isi ọkụ
  • Otutu punctures chọta veins
  • Hematoma (ọbara na-agbakọta n'okpuru anụ ahụ)
  • Ofufe Ọrịa (ntakịrị ihe egwu oge ọ bụla anụ ahụ agbajiri)

Ule a na-emekarị maka ndị nwere nsogbu ọbara ọgbụgba. Ihe ize ndụ nke nnukwu ọbara ọgbụgba dịtụ ukwuu maka ndị nwere nsogbu ọbara ọgbụgba karịa ndị ọzọ.


Ihe Plasma nke VIII antigen; Ihe Antihemophilia; AHF

Carcao M, Moorehead P, Lillicrap D. Hemophilia A na B. Na: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: ickpụrụ na Omume. Nke 7. Philadelphia, PA: Elsevier; 2018: isi 135.

Chernecky CC, Berger BJ. Ihe na-akpata VIII (ihe na-akpata antihemophilia, AHF) - ọbara. Na: Chernecky CC, Berger BJ, eds. Nnwale Laboratory na Usoro Nyocha. Nke isii. St Louis, MO: Elsevier Saunders; 2013: 504-505.

Napolitano M, Schmaier AH, Kessler CM. Coagulation na fibrinolysis. Na: McPherson RA, Pincus MR, eds. Henry’s Clinical Diagnosis and Management site na Labozọ Laboratory. 23 nke ed. St Louis, MO: Elsevier; 2017: isi 39.

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