Odee: William Ramirez
OfbọChị Okike: 18 Septemba 2021
DatebọChị Mmelite: 17 Juunu 2024
Anonim
Esophageal Atresia : Etiology, Types, Pathophysiology , Clinical Features , Diagnosis and Treatment
Vidio: Esophageal Atresia : Etiology, Types, Pathophysiology , Clinical Features , Diagnosis and Treatment

Esophageal atresia bụ nsogbu nri nke esophagus anaghị emepe nke ọma. Akpịrị akpịrị bụ ọkpọkọ nke na-ebukarị nri site n’ọnụ ruo n’afọ.

Atsosia nke Esophageal (EA) bụ nkwarụ ebumpụta ụwa. Nke a pụtara na ọ na-eme tupu amụọ nwa. E nwere ọtụtụ ụdị. N'ọtụtụ ọnọdụ, esophagus nke elu na-agwụ ma ghara ijikọta esophagus na afọ.

Imirikiti ụmụ ọhụrụ nwere EA nwere ntụpọ ọzọ a na-akpọ tracheoesophageal fistula (TEF). Nke a bụ njikọ na-adịghị mma n'etiti esophagus na windpipe (trachea).

Na mgbakwunye, ụmụ ọhụrụ nwere EA / TEF na-enwekarị tracheomalacia. Nke a bụ adịghị ike na nsị nke mgbidi windpipe, nke nwere ike ime ka iku ume na-ada ụda dị elu ma ọ bụ mkpọtụ.

Fọdụ ụmụ ọhụrụ nwere EA / TEF nwekwara ntụpọ ndị ọzọ, ọ na-abụkarị nkwarụ obi.

Mgbaàmà nke EA nwere ike ịgụnye:

  • Bluish coloration na anụ ahụ (cyanosis) na nwara nri
  • Ughkwara, iku ume, na ịkpagbu site na ịnwale nri
  • Iwe
  • Ogbenye nri

Tupu a mụọ ya, ultrasound nke nne nwere ike igosi oke mmiri ọmụmụ. Nke a nwere ike ịbụ ihe ịrịba ama nke EA ma ọ bụ ihe mgbochi ndị ọzọ nke tract digestive nwa.


N’oge na-adịghị anya a mụrụ nwa a, ọ na - achọpụta nsogbu ahụ mgbe nwa ọhụrụ nwaa n ’inye nri, ụkwara akwara, ma ọ bụ acha anụnụ anụnụ. Ọ bụrụ na a na-enyo EA enyo, onye nlekọta ahụike ga-anwa ịgafe obere obere nri site n'ọnụ nwa ọhụrụ ahụ ma ọ bụ imi ya n'ime afọ. Ọ bụrụ na ọkpọ nri anaghị enwe ike ịgafe afọ niile, enwere ike ịchọpụta nwa ọhụrụ na EA.

Mgbe ahụ, a na-eme x-ray, ọ ga-egosikwa nke ọ bụla n'ime ihe ndị a:

  • Akpa jupụta ikuku na akpịrị.
  • Ikuku n'ime afo na eriri afọ.
  • Akpa nri ga-apụta na-agbakọta na esophagus elu ma ọ bụrụ na etinyere ya tupu x-ray.

EA bụ mberede ịwa ahụ. Wa ahụ iji rụzie esophagus na-eme ngwa ngwa o kwere omume mgbe amuchara nwa ka ngụgụ ghara imebi na nwata nwere ike nye nri.

Tupu ịwa ahụ, nwa ahụ anaghị eri nri, ọ ga-achọ nri nri intravenous (IV). A na-elezi anya iji gbochie njem nke ikuku ume na ngụgụ.

Nchoputa nke mbu na-enye ohere di nma nke ezi ihe.


Nwatakịrị ahụ nwere ike iku ume mmiri na mmiri ndị ọzọ na ngụgụ, na-ebute oyi baa mmadụ, iku ume, na ikekwe nwụọ.

Nsogbu ndị ọzọ nwere ike ịgụnye:

  • Nsogbu nri
  • Reflux (na-ebugharị nri site na afọ) mgbe ịwachara ahụ
  • Narrowing (nlezianya) nke esophagus n'ihi ụcha ịwa ahụ

Matkọcha oge nwere ike ime ka ọnọdụ ahụ sie ike. Dịka e kwuru n'elu, enwere ike inwe ntụpọ n'akụkụ ndị ọzọ nke ahụ.

A na-achọpụta ọrịa a n'oge na-adịghị anya mgbe amuchara nwa.

Kpọọ onye na-enye nwa gị ozugbo ọ bụrụ na nwa agbaa ya ugboro ugboro mgbe enyechara ya nri, maọbụ ọ bụrụ na nwa ahụ enwee nsogbu iku ume.

Madanick R, Orlando RC. Ọdịdị, akụkọ ihe mere eme, embryology, na mmepe anomalies nke esophagus. Na: Feldman M, Friedman LS, Brandt LJ, eds. Sleisenger na Ọrịa Cancer nke Fordtran na Ọrịa Imeju: Pathophysiology / Diagnosis / Management. Nke iri. Philadelphia, PA: Elsevier Saunders; 2016: isi 42.

Rothenberg nke abụọ. Atopia nke Essophageal na tracheoesophageal fistula malformations. Na: Holcomb GW, Murphy JP, St. Peter SD, eds. Holcomb na craftwa Ahụ ụmụaka nke Ashcraft. Nke 7. Philadelphia, PA: Elsevier Saunders; 2020: isi 27.


Wolf RB. Ime onyonyo. Na: Resnik R, Lockwood CJ, Moore TR, Greene MF, Copel JA, Silver RM, eds. Nkà Mmụta Nne na Nwa nke Creasy na Resnik: Prinkpụrụ na Omume. 8th ed. Philadelphia, PA: Elsevier Saunders; 2019: isi 26.

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