Tetralogy nke Fallot

Tetralogy nke Fallot bụ ụdị nkwarụ obi congenital. Congenital pụtara na ọ dị n'oge a na-amụ nwa.

Tetralogy nke Fallot na - akpata ikuku oxygen dị n’ọbara. Nke a na - eduga na cyanosis (ụcha bluish-purple purple skin).

Dị nke oge gboo nwere ntụpọ anọ nke obi na nnukwu arịa ọbara ya:

• Ventricular septal ntụpọ (oghere n'etiti aka nri na aka ekpe)
• Na-agbachi usoro ikuku akpa ume (valvụ na akwara nke jikọtara obi na ngụgụ)
• Na-ekpuchi aorta (akwara nke na-ebu ọbara oxygen na anụ ahụ) nke a gbanwere n'akụkụ aka nri aka ya na ntụpọ oghere ventricular, kama ịpụta naanị site na ventricle aka ekpe
• Mgbidi siri ike nke ventricle ziri ezi (hypertrophy nke aka nri)

Tetralogy nke Fallot dị obere, mana ọ bụ ụdị ọrịa obi na-ebutekarị cyanotic. Ọ na-adịkarị otu nwoke na nwanyị. Ndi mmadu nwere tetralogy nke Fallot nwekwara ike inwe nsogbu ndi ozo.

A maghị ihe kpatara ọtụtụ nkwarụ obi na-efe efe. Ọtụtụ ihe yiri ka ọ bụ ihe metụtara.

Ihe ndị na - eme ka ọnọdụ a dị njọ n’oge afọ ime gụnyere:

• Mmanya na-egbu egbu na nne
• Ọrịa shuga
• Mama karịrị afọ iri anọ
• Ihe oriri na-edozi ahụ n'oge afọ ime
• Rubella ma ọ bụ ọrịa nje ndị ọzọ n'oge ime ime

Childrenmụaka nwere tetralogy nke Fallot nwere ike ịnwe ọrịa chromosome, dịka Down syndrome, Alagille syndrome, na DiGeorge syndrome (ọnọdụ nke na-akpata nkwarụ obi, obere calcium, na arụ ọrụ adịghị mma).

Mgbaàmà gụnyere:

• Colorcha acha anụnụ anụnụ na anụ ahụ (cyanosis), nke na-akawanye njọ mgbe nwa ahụ na-ewe iwe
• Mkpịsị aka mkpịsị aka (akpụkpọ ahụ ma ọ bụ ịmụba ọkpụkpụ gburugburu mbọ aka)
• Nri nri (nri nri adịghị mma)
• Enweghị ike iburu ibu
• Na-agafe
• Mmebi adịghị mma
• Squatting n'oge ngosipụta nke cyanosis

Nnwale anụ ahụ na stethoscope na-ekpughekarị ntamu obi.

Ule nwere ike ịgụnye:

• Igbe x-ray
• Ọnụọgụ ọbara zuru ezu (CBC)
• Ihe omumu
• Nchịkwa Electrocardiogram (ECG)
• MRI nke obi (n'ozuzu mgbe ịwachara ahụ)
• CT nke obi

Gerywa ahụ iji rụkwaa tetralogy nke Fallot na-eme mgbe nwa ọhụrụ ahụ dị obere, ọ kachasị tupu ọnwa isii. Mgbe ụfọdụ, a na-achọ ihe karịrị otu ịwa ahụ. Mgbe ejiri ihe karịrị otu ịwa ahụ, a na-eme ịwa ahụ mbụ iji nyere aka mee ka ọbara na-erugharị na ngụgụ.

Wa ahụ iji dozie nsogbu ahụ nwere ike ịme n'oge ọzọ. Ọtụtụ mgbe naanị otu ịwa ahụ na-edozi ahụ na-arụ na ọnwa ole na ole nke ndụ. A na-arụ ọrụ ịwa ahụ iji mepee akụkụ nke eriri akpa ahụ dị warara ma mechie ntụpọ oghere nke oghere na oghere.

Ọtụtụ ikpe nwere ike idozi ya na ịwa ahụ. Iesmụ ọhụrụ ndị a na-awa ahụ na-agakarị nke ọma. Ihe kariri 90% na-adi ndu rue ndu ma bie ndu, nke siri ike, ma na-aruta oru. Enweghị ịwa ahụ, ọnwụ na-abịakarị tupu mmadụ eruo afọ iri abụọ.

Ndị mmadụ gara n’ihu, ịdị ike ike nke eriri akpa ume nwere ike ịchọ ka edochi valvụ ahụ.

A na-atụ aro ka a na-esochi ndị na-ahụ maka ọrịa anya mgbe niile.

Nsogbu nwere ike ịgụnye:

• Igbu oge na mmepe
• Oge ufodu obi (arrhythmias)
• Na-ejide ihe n’oge oge ikuku oxygen adịghị ezu
• Ọnwụ site na njide ejiri obi, ọbụlagodi mgbe emechara ịwa ahụ

Kpọọ onye na-ahụ maka ahụike gị ma ọ bụrụ na mgbaàmà ọhụụ akọwabeghị amalite ma ọ bụ nwata ahụ nwere nsogbu nke cyanosis (acha anụnụ anụnụ).

Ọ bụrụ na nwatakịrị nwere tetralogy nke Fallot na-acha anụnụ anụnụ, tinye nwa ahụ ozugbo n'akụkụ ya ma ọ bụ azụ ya ma tinye ikpere ruo n'obi. Mee ka nwa ahụ dị jụụ ma chọọ nlekọta ahụike ozugbo.

Onweghi uzo a mara iji gbochie onodu a.

Tet; TOF; Congenital obi nkwarụ - tetralogy; Ọrịa obi Cyanotic - tetralogy; Omumu omumu - tetralogy

• Surgerywa ahụ obi ụmụaka - ihapu

• Obi - ngalaba site n'etiti
• Tetralogy nke Fallot
• Cyanotic 'Tet okwu'

Bernstein D. Cyanotic congenital ọrịa obi: nwalere onye na-arịa ọrịa dị egwu nke nwere cyanosis na nsogbu iku ume. Na: Kliegman RM, Stanton BF, St Geme JW, Schor NF, ndị ọzọ. Nelson Akwụkwọ ọgụgụ nke Ọrịa edimụaka. 21nke ed. Philadelphia, PA: Elsevier; 2019: isi 456.

Fraser CD, Kane LC. Ọrịa afọ ime. Na: Townsend CM Jr, Beauchamp RD, Evers BM, Mattox KL, eds. Akwụkwọ Sabiston nke gerywa Ahụ: Ntọala Nduzi nke Omume Ahụhụ Oge a. Agba nke 20. Philadelphia, PA: Elsevier; 2017: isi 58.

Webb GD, Smallhorn JF, Therrien J, Redington AN. Congenital ọrịa obi na okenye na ụmụaka na-enwe ndidi. Na: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. Ọrịa Obi Braunwald: Akwụkwọ ọgụgụ nke Ọgwụ Ọrịa Cardiovascular. Nke 11. Philadelphia, PA: Elsevier; 2019: isi 75.